Medicine:Mediastinal fibrosis

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Mediastinal fibrosis
Autosomal recessive - en.svg
Mediastinal fibrosis is inherited in an autosomal recessive manner
SpecialtyPulmonology
Causeshistoplasmosis
Treatmentglucocorticoids or immunosuppressants[1]

Mediastinal fibrosis is characterized by invasive, calcified fibrosis centered on lymph nodes that block major vessels and airways. In Europe, this disease is exceptionally rare. More cases are seen in USA where the disease may often be associated with histoplasmosis.[2][3]

See also

References

  1. Rossi, Giovanni M.; Emmi, Giacomo; Corradi, Domenico; Urban, Maria L.; Maritati, Federica; Landini, Federica; Galli, Paola; Palmisano, Alessandra et al. (June 2017). "Idiopathic Mediastinal Fibrosis: a Systemic Immune-Mediated Disorder. A Case Series and a Review of the Literature". Clinical Reviews in Allergy & Immunology 52 (3): 446–459. doi:10.1007/s12016-016-8584-1. PMID 27553003. 
  2. "Mediastinal fibrosis". Seminars in Respiratory Infections 16 (2): 119–30. 2001. doi:10.1053/srin.2001.24242. PMID 11521244. 
  3. "Surgical treatment of idiopathic mediastinal fibrosis: report of five cases". Thorax 41 (3): 210–4. 1986. doi:10.1136/thx.41.3.210. PMID 3715778. 

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