Medicine:Raymond–Céstan syndrome

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Raymond–Céstan syndrome
Other namesupper dorsal pontine syndrome,
Circle of Willis en.svg
Basillar artery runs down the middle(in above image) and blockage is cause of this condition. Diagram of the arterial circulation at the base of the brain (inferior view).
Diagnostic methodCect/ncct brain, mri brain

Raymond–Céstan syndrome is caused by blockage of the long circumferential branches of the basilar artery.[1] It was described by Fulgence Raymond and Étienne Jacques Marie Raymond Céstan.[2] Along with other related syndromes such as Millard–Gubler syndrome, Foville's syndrome, and Weber's syndrome, the description was instrumental in establishing important principles in brain-stem localization.[3]

Presentation

  • Ipsilateral ataxia and coarse intention tremor (damage to superior and middle cerebellar peduncle)
  • Ipsilateral paralysis of muscles of mastication and sensory loss in face (damage to sensory and motor nuclei and tracts of CN V)
  • Contralateral loss of sensory modalities in the body (damage to spinothalamic tract and medial lemniscus)
  • Contralateral hemiparesis of face and body (damage to corticospinal tract) may occur with ventral extension of lesion
  • Horizontal gaze palsy may occur (as in lower dorsal pontine syndrome)

Diagnosis

Treatment

References

  1. http://www.clineu-journal.com/article/S0303-8467(07)00181-3/abstract
  2. "Céstan-Chenais syndrome". http://www.whonamedit.com/synd.cfm/618.html. 
  3. Silverman, IE; Liu, GT; Volpe, NJ; Galetta, SL (June 1995). The crossed paralyses. The original brain-stem syndromes of Millard-Gubler, Foville, Weber, and Raymond-Cestan. Archives of Neurology. 52. pp. 635–8. doi:10.1001/archneur.1995.00540300117021. PMID 7763214. 

Further reading

  • Kim, JS; Lee, JH; Im, JH; Lee, MC (Jun 1995). "Syndromes of pontine base infarction. A clinical-radiological correlation study.". Stroke: A Journal of Cerebral Circulation 26 (6): 950–5. doi:10.1161/01.STR.26.6.950. PMID 7762044. 
  • Krasnianski, M; Neudecker, S; Zierz, S (Aug 2004). "[Classical crossed pontine syndromes]." (in German). Fortschritte der Neurologie · Psychiatrie 72 (8): 460–8. doi:10.1055/s-2004-818392. PMID 15305240.